Rosette-forming glioneuronal tumour of the fourth ventricle: case report and review of the literature.
نویسندگان
چکیده
Rosette-forming glioneuronal tumour (RGNT) of the fourth ventricle is one of the newly described primary tumours of the central nervous system. These tumours have two components of both neurocytic and glial areas but usually the glial component of the tumour predominates. They have biphasic cytoarchitecture with two elements; neurocytic rosettes resembling Homer-Wright rosettes, and astrocytic component resembling a pilocytic astrocytoma. They are low-grade tumours with lack of histopathological signs of malignancy. Here, clinical, magnetic resonance, computed tomography (CT) and pathological features of rosette-forming glioneuronal tumour of posterior fossa are presented. A 29-year-man was admitted with an acute neurological deterioration. A three ventricular hydrocephalus and a hypo-density around vermis in the posterior fossa were seen in his CT scans. He did well after an emergency external ventricular drainage. He had an elective operation and a mass that was reported to be a rosette-forming glioneuronal tumour of the fourth ventricle was excised.
منابع مشابه
Papillary glioneuronal tumor of the fourth ventricle: case report and review of the literature.
Rosette-forming glioneuronal tumour (RGNT) of the fourth ventricle is a relatively new entity recently described. Neuronal and mixed neuronal-glial tumours have been incorporated in the same category in the WHO Classification of Nervous System Tumours. This category comprises heterogeneous neoplasms composed of neuronal and glial cells with various grades of differentiation. We present a case o...
متن کاملRosette-forming glioneuronal tumour: imaging features, histopathological correlation and a comprehensive review of literature.
BACKGROUND Rosette-forming glioneuronal tumour (RGNT) is a rare and novel brain tumour. We present a case of rosette forming glioneuronal tumour of the fourth ventricle and highlight the imaging and histological features of this tumour entity. We also performed a comprehensive review of the imaging features, treatments and outcomes of all past cases and make recommendations on diagnosis and man...
متن کاملClinical implications of the infratentorial rosette-forming glioneuronal tumor: case report.
OBJECTIVE This article describes our experience with two patients who presented with unusual tumors in the cerebellar vermis and cerebral aqueduct. Although sparing the fourth ventricle proper, both tumors had histological features consistent with the rare diagnosis of a rosette-forming glioneuronal tumor of the fourth ventricle, of which only 19 cases have been reported previously. A review of...
متن کاملThe expanding family of glioneuronal tumors.
Three new entities have been recently added to the group of glioneuronal tumors in the most recent update of the World Health Organization classification of tumors of the central nervous system: papillary glioneuronal tumor, rosetted glioneuronal tumor with neuropil-like islands, and rosette-forming glioneuronal tumor of the fourth ventricle. These tumors are relatively infrequent lesions, and ...
متن کاملThe 2007 WHO Classification of Nervous System Tumors: newly recognized members of the mixed glioneuronal group.
The clinical and pathologic features of two glioneuronal neoplasms newly incorporated in the 2007 revision of the WHO classification of nervous system tumors are reviewed. These are the papillary glioneuronal tumor and the rosette-forming glioneuronal tumor of the fourth ventricle.
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Folia neuropathologica
دوره 54 1 شماره
صفحات -
تاریخ انتشار 2016